Registry to evaluate early and long-term disease management in PAH (REVEAL)

Pulmonary artery hypertension (PAH) is a condition with significant clinical symptoms, poor quality of life and early mortality. Heath-Edwards classification which was based primarily on pulmonary vascular histology changes include a spectrum of lesions like vasoconstriction, intimal hyperplasia, medial hypertrophy, plexiform arteriopathy, perivascular inflammation, and thrombotic lesions within the pulmonary vasculature (1-3).